Coxa vara: a rare but important condition

Clinical Cases 08.02.2003
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Section: Musculoskeletal system
Case Type: Clinical Cases
Patient: 10 years, male
Authors: C. Simpson, Z. Abiddin, C.E. Bruce
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AI Report

Clinical History

Left-sided limp of a few years' duration in a patient with limited abduction of the hip.

Imaging Findings

The patient presented with a history of a left-sided limp of a few years' duration. The patient had no associated symptoms and took part in all normal physical activities.

On examination he had a limb length discrepancy of 1.5cm on the left side. The leg had a full range of flexion, internal and external rotation, but had a reduced range of abduction to 30 degrees on the left as compared with 45 degrees on the right side.

A pelvic radiograph demonstrated typical coxa vara with a neck shaft angle of between 90 and 100 degrees (Fig. 1).

Discussion

Coxa vara was first described by Fiorini in 1881. This rare deformity of the hip tends to present in early childhood with concerns regarding a limp. This may be associated with a reduced range of movement of the hip joint, especially abduction and internal rotation (1).

It is bilateral in one third to one half of cases. Coxa vara can be congenital (noted at birth and differentiated from developmental dysplasia of the hip by MRI), developmental (AD, progressive), or acquired (e.g. trauma, Perthes disease, slipped capital femoral epiphysis).

Carroll described it as a decrease in the neck shaft angle to less than 110 degrees (2).

On radiographs it is characterised by a reduction in the neck shaft angle, with the physeal plate being in a vertical position and a triangular metaphyseal fragment being visible in the inferior part of femoral neck (Fairbanks triangle). The fragment is surrounded by an inverted Y pattern (1).

There have been multiple attempts to classify this condition radiologically, however it is not possible to rely on any of these signs for early management decisions (3).

Treatment of the condition aims at normalising the forces across the proximal femoral epiphysis, from shearing forces in coxa vara to compressive forces (2,4). This is performed by doing a corrective osteotomy (Fig. 3). In reviews, the most reliable predictor of progression and recurrence post-operatively was found to be Hilgenreiner's epiphyseal angle (2,5). This is determined by the use of Hilgenreiner's line as the horizontal axis, with a line through the defect adjacent to the metaphyseal axis (5).

Weinstein (5) found that coxa vara progressed if Hilgenreiner's angle was greater than 60 degrees, whereas there was spontaneous correction if the angle measured less than 45 degrees. For a surgical correction to be successful, it was demonstrated necessary to obtain Hilgenreiner's angle of less than 38 degrees. Cases with angles greater than 40 degrees required revision surgery for recurrence.

The functional and radiological results were found to be good in 95% of cases when correction was obtained before the age of 10 years (2).

Differential Diagnosis List

Coxa vara of the left hip

Final Diagnosis

Coxa vara of the left hip

Liscense

Figures

AP view of the pelvis

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AP view of the pelvis

AP view of the pelvis

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AP view of the pelvis

Post-operative AP view of the left hip

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Post-operative AP view of the left hip